Angiosarkom pravé síně

Heart tumors represent a relatively rare but serious group of cardiovascular disorders with late development of a wide scale of symptoms, the correct and timely diagnosis of which is still challenging. Malignant heart tumors are usually located in right-sided heart cavities but their incidence is very low. We describe a case of right atrial angiosarcoma, manifesting initially with a dyspnea and syncope during cardiac tamponade. After an emergent surgical procedure and favorable postoperative development, the patient underwent adjuvant chemotherapy. He has been clinically stabilized and symptom-free for 8 months, followed by disease recurrence with metastatic involvement of the right lung, liver, pericardium and lymph nodes leading to his death. We offer a description of a complete typical course of a rare oncologic disease with a cardiac symptomatology, notable especially for its differential diagnostic aspects.