Perspectives on holoprosencephaly: Part III. Spectra, distinctions, continuities, and discontinuities

Résultat de recherche: Review articleexamen par les pairs

199 Citations (Scopus)

Résumé

This attemps to balance our knowledge of holoprosencephalic spectra and continuities with important distinctions and discontinuities. Prevalence studies and syndrome delineation are briefly reviewed. The following topics receive detailed coverage: human teratogens, special aspects of forebrain and hindbrain malformations, aprosencephaly/atelencephaly, association with neural tube defects, current assessment of 'facial principles', and endocrine abnormalities.

Langue d'origineEnglish
Pages (de-à)271-288
Nombre de pages18
JournalAmerican Journal of Medical Genetics
Volume34
Numéro de publication2
DOI
Statut de publicationPublished - 1989

ASJC Scopus Subject Areas

  • Genetics(clinical)

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